A rare subtype of poems syndrome: IGG4 subtype
نویسندگان
چکیده
منابع مشابه
POEMS syndrome - a unique presentation of a rare paraneoplastic syndrome.
POEMS (peripheral neuropathy, organomegaly, endocrinopathy, M protein, skin changes) syndrome is a rare multisystem paraneoplastic disorder. A 40-year-old male with a history of peripheral neuropathy and erectile dysfunction presented with a pathological fracture of the neck of the femur, found to be a solitary plasmacytoma. Additional unusual features included splenomegaly, hyperprolactinaemia...
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We report a case of granulomatous slack skin, a rare and indolent subtype of mycosis fungoides. It affects mainly men between the third and fourth decades. It is characterized by hardened and erithematous plaques that mainly affect flexural areas and become pedunculated after some years. Histological examination shows a dense infiltrate of small atypical lymphocytes involving the dermis (and so...
متن کاملA rare cause of pericardial effusion and ascites: POEMS syndrome
POEMS syndrome is an important paraneoplastic syndrome associated with multisystem involvement. Extravascular volume overload like pericardial effusion and ascites has a broad differential diagnosis. In addition, it may be initial presentation of disease. For that reason, this case report is highlight to warn of different forms of presentation of poems syndrome.
متن کاملWhat is IgG4? A review of the biology of a unique immunoglobulin subtype.
PURPOSE OF REVIEW Recent descriptions of the group of clinical disorders collectively defined as IgG4-related systemic disease (IgG4-RSD) have prompted this review of the unique biology of the IgG4 antibody. This article will discuss IgG4 structure and function, the unique phenomenon of half-antibody exchange, and the implications of IgG4 biology for its proposed role in immunologic diseases. ...
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ژورنال
عنوان ژورنال: Hematology, Transfusion and Cell Therapy
سال: 2020
ISSN: 2531-1379
DOI: 10.1016/j.htct.2020.09.095